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Atorvastatin counteracts aberrant soft tissue mineralization in a mouse model of pseudoxanthoma elasticum (Abcc6(−/−))

Pseudoxanthoma elasticum (PXE), a multisystem heritable disorder with aberrant mineralization of arterial blood vessels, is caused by mutations in the ABCC6 gene. Previous studies have suggested that carriers of the ABCC6 mutations, particularly of p.R1141X, are at increased risk for coronary artery...

Täydet tiedot

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Bibliografiset tiedot
Päätekijät: Guo, Haitao, Li, Qiaoli, Chou, David W., Uitto, Jouni
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2013
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC3783622/
https://ncbi.nlm.nih.gov/pubmed/23807484
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00109-013-1066-5
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