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Over-Expression of Fetuin-A Counteracts Ectopic Mineralization in a Mouse Model of Pseudoxanthoma Elasticum (Abcc6(−/−))

The pathologic hallmark of pseudoxanthoma elasticum (PXE) is ectopic mineralization of soft connective tissues. Recent studies have suggested that PXE is a metabolic disease, and perturbations in a number of circulatory factors have been postulated. One of them is fetuin-A, a 60-kDa glycoprotein syn...

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Autori principali: Jiang, Qiujie, Dibra, Florian, Lee, Michael D., Uitto, Jouni
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2891093/
https://ncbi.nlm.nih.gov/pubmed/20090764
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/jid.2009.423
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