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Disease-relevant proteostasis regulation of cystic fibrosis transmembrane conductance regulator

Mismanaged protein trafficking by the proteostasis network contributes to several conformational diseases, including cystic fibrosis, the most frequent lethal inherited disease in Caucasians. Proteostasis regulators, as cystamine, enable the beneficial action of cystic fibrosis transmembrane conduct...

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Bibliografiske detaljer
Main Authors: Villella, V R, Esposito, S, Bruscia, E M, Vicinanza, M, Cenci, S, Guido, S, Pettoello-Mantovani, M, Carnuccio, R, De Matteis, M A, Luini, A, Maiuri, M C, Raia, V, Kroemer, G, Maiuri, L
Format: Artigo
Sprog:Inglês
Udgivet: Nature Publishing Group 2013
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3705602/
https://ncbi.nlm.nih.gov/pubmed/23686137
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/cdd.2013.46
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