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Cytoplasmic aggregates trap polyglutamine-containing proteins and block axonal transport in a Drosophila model of Huntington's disease

Huntington's disease is an autosomal dominant neurodegenerative disorder caused by expansion of a polyglutamine tract in the huntingtin protein that results in intracellular aggregate formation and neurodegeneration. Pathways leading from polyglutamine tract expansion to disease pathogenesis re...

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Autori principali: Lee, Wyan-Ching Mimi, Yoshihara, Motojiro, Littleton, J. Troy
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2004
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC365771/
https://ncbi.nlm.nih.gov/pubmed/14978262
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0400243101
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