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Gradual processing of the ITS1 from the nucleolus to the cytoplasm during synthesis of the human 18S rRNA

Defects in ribosome biogenesis trigger stress response pathways, which perturb cell proliferation and differentiation in several genetic diseases. In Diamond–Blackfan anemia (DBA), a congenital erythroblastopenia, mutations in ribosomal protein genes often interfere with the processing of the intern...

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Dettagli Bibliografici
Autori principali: Preti, Milena, O'Donohue, Marie-Françoise, Montel-Lehry, Nathalie, Bortolin-Cavaillé, Marie-Line, Choesmel, Valérie, Gleizes, Pierre-Emmanuel
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2013
Soggetti:
RNA
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3632142/
https://ncbi.nlm.nih.gov/pubmed/23482395
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/nar/gkt160
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