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XBP1 Depletion Precedes Ubiquitin Aggregation and Golgi Fragmentation in TDP-43 Transgenic Rats

Protein inclusion is a prominent feature of neurodegenerative diseases including frontotemporal lobar degeneration (FTLD) that is characterized by the presence of ubiquitinated TDP-43 inclusion. Presence of protein inclusions indicates an interruption to protein degradation machinery or the overload...

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Detalhes bibliográficos
Main Authors: Tong, Jianbin, Huang, Cao, Bi, Fangfang, Wu, Qinxue, Huang, Bo, Zhou, Hongxia
Formato: Artigo
Idioma:Inglês
Publicado em: 2012
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3534861/
https://ncbi.nlm.nih.gov/pubmed/22970712
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/jnc.12014
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