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Acid Sphingomyelinase Deficiency Contributes to Resistance of Scleroderma fibroblasts to Fas-mediated Apoptosis
BACKGROUND: Scleroderma (SSc) is characterized by excess production and deposition of extracellular matrix (ECM) proteins. Activated fibroblasts play a key role in fibrosis in SSc. and are resistant to Fas-mediated apoptosis. Acid Sphingomyelinase (ASMase), a major sphingolipid enzyme, plays an impo...
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| Main Authors: | , , , , |
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| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
2012
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3423203/ https://ncbi.nlm.nih.gov/pubmed/22771321 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jdermsci.2012.06.001 |
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