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Pulmonary alveolar proteinosis: diagnostic and therapeutic challenges

Pulmonary Alveolar Proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces. It occurs with a reported prevalence of 0.1 per 100,000 individuals and in distinct clinical forms: autoimmune (previously referred to as the idiopathic form, repres...

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Detalles Bibliográficos
Main Authors: Campo, Ilaria, Kadija, Zamir, Mariani, Francesca, Paracchini, Elena, Rodi, Giuseppe, Mojoli, Francesco, Braschi, Antonio, Luisetti, Maurizio
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2012
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3415123/
https://ncbi.nlm.nih.gov/pubmed/22958344
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/2049-6958-7-4
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