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Pulmonary alveolar proteinosis: from classification to therapy

Pulmonary alveolar proteinosis (PAP) is a rare respiratory syndrome characterised by the accumulation of surfactant lipoproteins within the alveoli. According to various pathogenetic mechanisms and aetiologies, PAP is classified as primary, secondary or congenital. Primary PAP is led by a granulocyt...

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Podrobná bibliografie
Vydáno v:Breathe (Sheff)
Hlavní autoři: Salvaterra, Elena, Campo, Ilaria
Médium: Artigo
Jazyk:Inglês
Vydáno: European Respiratory Society 2020
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC7341616/
https://ncbi.nlm.nih.gov/pubmed/32684997
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/20734735.0018-2020
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