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Assessment and management of pulmonary alveolar proteinosis in a reference center

Pulmonary alveolar proteinosis (PAP) is a term defining an ultra-rare group of disorders characterised by a perturbation in surfactant homeostasis, resulting in its accumulation within airspaces and impaired gas transfer. In this report we provide data from a cohort of PAP patients (n = 81) followed...

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Detalhes bibliográficos
Main Authors: Campo, Ilaria, Mariani, Francesca, Rodi, Giuseppe, Paracchini, Elena, Tsana, Eric, Piloni, Davide, Nobili, Isabella, Kadija, Zamir, Corsico, Angelo, Cerveri, Isa, Chalk, Claudia, Trapnell, Bruce C, Braschi, Antonio, Tinelli, Carmine, Luisetti, Maurizio
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2013
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3605309/
https://ncbi.nlm.nih.gov/pubmed/23497546
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1750-1172-8-40
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