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A proteasome inhibitor fails to attenuate dystrophic pathology in mdx mice

Dystrophin deficiency leads to increased proteasome activity in skeletal muscle. Previous observations suggest short-term inhibition of the proteasome restores dystrophin expression. Contrary to our hypothesis, eight days of MG-132 administration to mdx mice increased susceptibility to contraction i...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Selsby, Joshua, Morris, Carl, Morris, Linda, Sweeney, Lee
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Public Library of Science 2012
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3392143/
https://ncbi.nlm.nih.gov/pubmed/22866241
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/4f84a944d8930
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