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Expression of the inclusion body myopathy 3 mutation in Drosophila depresses myosin function and stability and recapitulates muscle inclusions and weakness

Hereditary myosin myopathies are characterized by variable clinical features. Inclusion body myopathy 3 (IBM-3) is an autosomal dominant disease associated with a missense mutation (E706K) in the myosin heavy chain IIa gene. Adult patients experience progressive muscle weakness. Biopsies reveal dyst...

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Detalhes bibliográficos
Main Authors: Wang, Yang, Melkani, Girish C., Suggs, Jennifer A., Melkani, Anju, Kronert, William A., Cammarato, Anthony, Bernstein, Sanford I.
Formato: Artigo
Idioma:Inglês
Publicado em: The American Society for Cell Biology 2012
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3364171/
https://ncbi.nlm.nih.gov/pubmed/22496423
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1091/mbc.E12-02-0120
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