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Regional deficiencies in chaperone-mediated autophagy underlie α-synuclein aggregation and neurodegeneration

In neurodegenerative diseases, it remains unclear why certain brain regions are selectively vulnerable to protein aggregation. In transgenic mice expressing human A53T α-synuclein, the brainstem and spinal cord develop the most prominent α-synuclein inclusions which correlate with age-dependent moto...

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Autores principales: Malkus, Kristen A., Ischiropoulos, Harry
Formato: Artigo
Lenguaje:Inglês
Publicado: 2012
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3352979/
https://ncbi.nlm.nih.gov/pubmed/22426402
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nbd.2012.03.017
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