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Redox signalling directly regulates TDP-43 via cysteine oxidation and disulphide cross-linking
TDP-43 is the major disease protein in ubiquitin-positive inclusions of amyotrophic lateral sclerosis and frontotemporal lobar degeneration (FTLD) characterized by TDP-43 pathology (FTLD-TDP). Accumulation of insoluble TDP-43 aggregates could impair normal TDP-43 functions and initiate disease progr...
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| Autori principali: | , , , , |
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| Natura: | Artigo |
| Lingua: | Inglês |
| Pubblicazione: |
Nature Publishing Group
2012
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| Soggetti: | |
| Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3297986/ https://ncbi.nlm.nih.gov/pubmed/22193716 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/emboj.2011.471 |
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