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The RAG2 C-terminus suppresses genomic instability and lymphomagenesis

Misrepair of DNA double-strand breaks (DSBs) produced by the V(D)J recombinase (the RAG1/RAG2 proteins) at immunoglobulin (Ig) and T cell receptor (Tcr) loci has been implicated in pathogenesis of lymphoid malignancies in humans(1) and in mice(2–7). Defects in DNA damage response factors such as ATM...

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Autors principals: Deriano, Ludovic, Chaumeil, Julie, Coussens, Marc, Multani, Asha, Chou, YiFan, Alekseyenko, Alexander V., Chang, Sandy, Skok, Jane A., Roth, David B.
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3174233/
https://ncbi.nlm.nih.gov/pubmed/21368836
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/nature09755
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