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P0S63del impedes the arrival of wild-type P0 glycoprotein to myelin in CMT1B mice

More than 120 mutations in the Myelin Protein Zero gene (MPZ, P0) cause various forms of hereditary neuropathy. Two human mutations encoding either P0S63C or P0S63del have been shown to cause demyelination in mice through different gain of function pathomechanisms. P0S63del, for example, is retained...

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Bibliografske podrobnosti
Main Authors: Fratta, Pietro, Saveri, Paola, Zambroni, Desiree, Ferri, Cinzia, Tinelli, Elisa, Messing, Albee, D'Antonio, Maurizio, Feltri, Maria Laura, Wrabetz, Lawrence
Format: Artigo
Jezik:Inglês
Izdano: Oxford University Press 2011
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC3090187/
https://ncbi.nlm.nih.gov/pubmed/21363884
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddr081
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