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Pseudoxanthoma Elasticum: A Streamlined, Ethnicity‐based Mutation Detection Strategy

Pseudoxanthoma elasticum (PXE), an autosomal recessive multisystem disorder, is caused by mutations in the ABCC6 gene, and approximately 300 distinct mutations representing >1,000 mutant alleles have been disclosed thus far. Few population‐based studies have reported mutational hotspots in some g...

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Autores principales: LaRusso, Jennifer, Ringpfeil, Franziska, Uitto, Jouni
Formato: Artigo
Lenguaje:Inglês
Publicado: Blackwell Publishing Inc 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3076205/
https://ncbi.nlm.nih.gov/pubmed/21167005
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1752-8062.2010.00243.x
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