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Pseudoxanthoma Elasticum, the Paradigm of Heritable Ectopic Mineralization Disorders - Can Diet Help?

Pseudoxanthoma elasticum (PXE) is a heritable multi-system disorder manifesting with characteristic cutaneous lesions, associated with ocular findings and cardiovascular involvement. The skin lesions, yellowish papules which coalesce into plaques of inelastic and leathery skin, demonstrate by histop...

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Autors principals: LaRusso, Jennifer, Li, Qiaoli, Uitto, Jouni
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3307339/
https://ncbi.nlm.nih.gov/pubmed/21435181
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1610-0387.2011.07658.x
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