Inhibition of Activin Receptor Type IIB Increases Strength and Lifespan in Myotubularin-Deficient Mice

X-linked myotubular myopathy (XLMTM) is a congenital disorder caused by deficiency of the lipid phosphatase, myotubularin. Patients with XLMTM often have severe perinatal weakness that requires mechanical ventilation to prevent death from respiratory failure. Muscle biopsy specimens from patients wi...

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Autori principali: Lawlor, Michael W., Read, Benjamin P., Edelstein, Rachel, Yang, Nicole, Pierson, Christopher R., Stein, Matthew J., Wermer-Colan, Ariana, Buj-Bello, Anna, Lachey, Jennifer L., Seehra, Jasbir S., Beggs, Alan H.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Investigative Pathology 2011
Soggetti:
Regular Article
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3069865/
https://ncbi.nlm.nih.gov/pubmed/21281811
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ajpath.2010.10.035
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