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Generation of a New Form of Human PrP(Sc) in Vitro by Interspecies Transmission from Cervid Prions

Prion diseases are infectious neurodegenerative disorders that affect humans and animals and that result from the conversion of normal prion protein (PrP(C)) into the misfolded prion protein (PrP(Sc)). Chronic wasting disease (CWD) is a prion disorder of increasing prevalence within the United State...

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Autori principali: Barria, Marcelo A., Telling, Glenn C., Gambetti, Pierluigi, Mastrianni, James A., Soto, Claudio
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Biochemistry and Molecular Biology 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3045004/
https://ncbi.nlm.nih.gov/pubmed/21209079
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M110.198465
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