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Dystrophin diagnosis: comparison of dystrophin abnormalities by immunofluorescence and immunoblot analyses.

Immunoblot characterization and immunofluorescence localization of dystrophin are presented for 76 human patients with various neuromuscular diseases. Normal dystrophin (shown by immunoblotting) was invariably visualized as a continuous, peripheral membrane immunostaining of myofibers. Biochemical a...

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Dades bibliogràfiques
Publicat a:Proc Natl Acad Sci U S A
Autors principals: Arahata, K, Hoffman, E P, Kunkel, L M, Ishiura, S, Tsukahara, T, Ishihara, T, Sunohara, N, Nonaka, I, Ozawa, E, Sugita, H
Format: Artigo
Idioma:Inglês
Publicat: National Academy of Sciences 1989
Matèries:
Accés en línia:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC298014/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/2674948/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.86.18.7154
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