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Dystrophin diagnosis: comparison of dystrophin abnormalities by immunofluorescence and immunoblot analyses.

Immunoblot characterization and immunofluorescence localization of dystrophin are presented for 76 human patients with various neuromuscular diseases. Normal dystrophin (shown by immunoblotting) was invariably visualized as a continuous, peripheral membrane immunostaining of myofibers. Biochemical a...

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Detalles Bibliográficos
Publicado en:Proc Natl Acad Sci U S A
Autores principales: Arahata, K, Hoffman, E P, Kunkel, L M, Ishiura, S, Tsukahara, T, Ishihara, T, Sunohara, N, Nonaka, I, Ozawa, E, Sugita, H
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 1989
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Acceso en línea:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC298014/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/2674948/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.86.18.7154
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