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Dystrophin diagnosis: comparison of dystrophin abnormalities by immunofluorescence and immunoblot analyses.

Immunoblot characterization and immunofluorescence localization of dystrophin are presented for 76 human patients with various neuromuscular diseases. Normal dystrophin (shown by immunoblotting) was invariably visualized as a continuous, peripheral membrane immunostaining of myofibers. Biochemical a...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Cyhoeddwyd yn:Proc Natl Acad Sci U S A
Prif Awduron: Arahata, K, Hoffman, E P, Kunkel, L M, Ishiura, S, Tsukahara, T, Ishihara, T, Sunohara, N, Nonaka, I, Ozawa, E, Sugita, H
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: National Academy of Sciences 1989
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC298014/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/2674948/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.86.18.7154
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