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Dystrophin diagnosis: comparison of dystrophin abnormalities by immunofluorescence and immunoblot analyses.

Immunoblot characterization and immunofluorescence localization of dystrophin are presented for 76 human patients with various neuromuscular diseases. Normal dystrophin (shown by immunoblotting) was invariably visualized as a continuous, peripheral membrane immunostaining of myofibers. Biochemical a...

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Detalhes bibliográficos
Publicado no:Proc Natl Acad Sci U S A
Principais autores: Arahata, K, Hoffman, E P, Kunkel, L M, Ishiura, S, Tsukahara, T, Ishihara, T, Sunohara, N, Nonaka, I, Ozawa, E, Sugita, H
Formato: Artigo
Idioma:Inglês
Publicado em: National Academy of Sciences 1989
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC298014/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/2674948/
https://ncbi.nlm.nih.govhttps://doi.org/10.1073/pnas.86.18.7154
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