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Huntingtin as an Essential Integrator of Intracellular Vesicular Trafficking

The neurodegenerative disorder Huntington’s Disease is caused by an expansion in the polyglutamine repeat region of the protein huntingtin. Multiple studies in cellular and animal model systems indicate that this mutation imparts a novel toxic function required for disease pathogenesis. However, hun...

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Autors principals: Caviston, Juliane P., Holzbaur, Erika L. F.
Format: Artigo
Idioma:Inglês
Publicat: 2009
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2930405/
https://ncbi.nlm.nih.gov/pubmed/19269181
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.tcb.2009.01.005
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