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Deficiency of Bloom syndrome helicase activity is radiomimetic

Bloom syndrome is caused by homozygous mutations in BLM, which encodes a RecQ DNA helicase. Patient-derived cells deficient in BLM helicase activity exhibit genetic instability—apparent cytogenetically as sister chromatid exchanges—and activated DNA damage signaling. In this report, we show that BLM...

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Hlavní autoři: Horowitz, David P., Topaloglu, Ozlem, Zhang, Yonggang, Bunz, Fred
Médium: Artigo
Jazyk:Inglês
Vydáno: 2008
Témata:
On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2891340/
https://ncbi.nlm.nih.gov/pubmed/18787401
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