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Cysteine 111 Affects Aggregation and Cytotoxicity of Mutant Cu,Zn-superoxide Dismutase Associated with Familial Amyotrophic Lateral Sclerosis

Converging evidence indicates that aberrant aggregation of mutant Cu,Zn-superoxide dismutase (mutSOD1) is strongly implicated in familial amyotrophic lateral sclerosis (FALS). MutSOD1 forms high molecular weight oligomers, which disappear under reducing conditions, both in neural tissues of FALS tra...

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Bibliografiset tiedot
Päätekijät: Cozzolino, Mauro, Amori, Ilaria, Grazia Pesaresi, Maria, Ferri, Alberto, Nencini, Monica, Teresa Carrì, Maria
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2007
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC2842925/
https://ncbi.nlm.nih.gov/pubmed/18006498
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M705657200
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