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Progressive synaptic pathology of motor cortical neurons in a BAC transgenic mouse model of Huntington’s Disease

Huntington’s disease (HD) is a neurodegenerative disorder caused by a polyglutamine repeat expansion in huntingtin. A newly developed BAC transgenic mouse model (BACHD) reproduces phenotypic features of HD including predominantly neuropil associated protein aggregation and progressive motor dysfunct...

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Autors principals: Spampanato, Jay, Gu, Xiaofeng, Yang, X. William, Mody, Istvan
Format: Artigo
Idioma:Inglês
Publicat: 2008
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2802129/
https://ncbi.nlm.nih.gov/pubmed/18854207
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.neuroscience.2008.09.020
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