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Proteotoxic stress increases nuclear localization of ataxin-3

Spinocerebellar ataxia type 3 (SCA3)/Machado Joseph disease results from expansion of the polyglutamine domain in ataxin-3 (Atx3). Atx3 is a transcriptional co-repressor, as well as a deubiquitinating enzyme that appears to function in cellular pathways involved in protein homeostasis. In this study...

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Autores principales: Reina, Christopher P., Zhong, Xiaoyan, Pittman, Randall N.
Formato: Artigo
Lenguaje:Inglês
Publicado: Oxford University Press 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2796889/
https://ncbi.nlm.nih.gov/pubmed/19843543
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddp482
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