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The polyglutamine neurodegenerative protein ataxin 3 regulates aggresome formation

The polyglutamine-containing neurodegenerative protein ataxin 3 (AT3) has deubiquitylating activity and binds ubiquitin chains with a preference for chains of four or more ubiquitins. Here we characterize the deubiquitylating activity of AT3 in vitro and show it trims/edits K48-linked ubiquitin chai...

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Autores principales: Burnett, Barrington G., Pittman, Randall N.
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2005
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC555481/
https://ncbi.nlm.nih.gov/pubmed/15767577
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0407252102
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