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A retrograde signal from RyR1 alters DHP receptor inactivation and limits window Ca(2+) release in muscle fibers of Y522S RyR1 knock-in mice

Malignant hyperthermia (MH) is a life-threatening hypermetabolic condition caused by dysfunctional Ca(2+) homeostasis in skeletal muscle, which primarily originates from genetic alterations in the Ca(2+) release channel (ryanodine receptor, RyR1) of the sarcoplasmic reticulum (SR). Owing to its phys...

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Detalhes bibliográficos
Main Authors: Andronache, Zoita, Hamilton, Susan L., Dirksen, Robert T., Melzer, Werner
Formato: Artigo
Idioma:Inglês
Publicado em: National Academy of Sciences 2009
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2657461/
https://ncbi.nlm.nih.gov/pubmed/19246389
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0812661106
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