Carregant...

Isovaleric Acidemia: New Aspects of Genetic and Phenotypic Heterogeneity

Isovaleric acidemia (IVA) is an autosomal recessive inborn error of leucine metabolism caused by a deficiency of the mitochondrial enzyme isovaleryl-CoA dehydrogenase (IVD) resulting in the accumulation of derivatives of isovaleryl-CoA. It was the first organic acidemia recognized in humans and can...

Descripció completa

Guardat en:
Dades bibliogràfiques
Autors principals: Vockley, Jerry, Ensenauer, Regina
Format: Artigo
Idioma:Inglês
Publicat: 2006
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2652706/
https://ncbi.nlm.nih.gov/pubmed/16602101
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajmg.c.30089
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!