A carregar...

Isovaleric Acidemia: New Aspects of Genetic and Phenotypic Heterogeneity

Isovaleric acidemia (IVA) is an autosomal recessive inborn error of leucine metabolism caused by a deficiency of the mitochondrial enzyme isovaleryl-CoA dehydrogenase (IVD) resulting in the accumulation of derivatives of isovaleryl-CoA. It was the first organic acidemia recognized in humans and can...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Main Authors: Vockley, Jerry, Ensenauer, Regina
Formato: Artigo
Idioma:Inglês
Publicado em: 2006
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2652706/
https://ncbi.nlm.nih.gov/pubmed/16602101
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/ajmg.c.30089
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!