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Metal Binding Domains 3 and 4 of the Wilson Disease Protein: Solution Structure and Interaction with the Copper(I) Chaperone HAH1

The Wilson disease protein or ATP7B is a P(1B)-type ATPase involved in human copper homeostasis. The extended N-terminus of ATP7B protrudes into the cytosol and contains six Cu(I) binding domains. This report presents the NMR structure of the polypeptide consisting of soluble Cu(I) binding domains 3...

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Autores principales: Banci, Lucia, Bertini, Ivano, Cantini, Francesca, Rosenzweig, Amy C., Yatsunyk, Liliya A.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2643083/
https://ncbi.nlm.nih.gov/pubmed/18558714
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/bi8004736
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