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A Point Mutation in Translation Initiation Factor 2B Leads to a Continuous Hyper Stress State in Oligodendroglial-Derived Cells

BACKGROUND: Mutations in eukaryotic translation initiation factor 2B (eIF2B) cause Childhood Ataxia with CNS Hypomyelination (CACH), also known as Vanishing White Matter disease (VWM). The disease is manifested by loss of brain myelin upon physiological stress. In a previous study, we showed that fi...

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Main Authors: Kantor, Liraz, Pinchasi, Dalia, Mintz, Michelle, Hathout, Yetrib, Vanderver, Adeline, Elroy-Stein, Orna
פורמט: Artigo
שפה:Inglês
יצא לאור: Public Library of Science 2008
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גישה מקוונת:https://ncbi.nlm.nih.gov/pmc/articles/PMC2583043/
https://ncbi.nlm.nih.gov/pubmed/19023445
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0003783
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