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A Point Mutation in Translation Initiation Factor 2B Leads to a Continuous Hyper Stress State in Oligodendroglial-Derived Cells

BACKGROUND: Mutations in eukaryotic translation initiation factor 2B (eIF2B) cause Childhood Ataxia with CNS Hypomyelination (CACH), also known as Vanishing White Matter disease (VWM). The disease is manifested by loss of brain myelin upon physiological stress. In a previous study, we showed that fi...

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Détails bibliographiques
Auteurs principaux: Kantor, Liraz, Pinchasi, Dalia, Mintz, Michelle, Hathout, Yetrib, Vanderver, Adeline, Elroy-Stein, Orna
Format: Artigo
Langue:Inglês
Publié: Public Library of Science 2008
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC2583043/
https://ncbi.nlm.nih.gov/pubmed/19023445
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0003783
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