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A Point Mutation in Translation Initiation Factor 2B Leads to a Continuous Hyper Stress State in Oligodendroglial-Derived Cells

BACKGROUND: Mutations in eukaryotic translation initiation factor 2B (eIF2B) cause Childhood Ataxia with CNS Hypomyelination (CACH), also known as Vanishing White Matter disease (VWM). The disease is manifested by loss of brain myelin upon physiological stress. In a previous study, we showed that fi...

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Autors principals: Kantor, Liraz, Pinchasi, Dalia, Mintz, Michelle, Hathout, Yetrib, Vanderver, Adeline, Elroy-Stein, Orna
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2008
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2583043/
https://ncbi.nlm.nih.gov/pubmed/19023445
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0003783
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