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A Point Mutation in Translation Initiation Factor 2B Leads to a Continuous Hyper Stress State in Oligodendroglial-Derived Cells

BACKGROUND: Mutations in eukaryotic translation initiation factor 2B (eIF2B) cause Childhood Ataxia with CNS Hypomyelination (CACH), also known as Vanishing White Matter disease (VWM). The disease is manifested by loss of brain myelin upon physiological stress. In a previous study, we showed that fi...

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Detalhes bibliográficos
Main Authors: Kantor, Liraz, Pinchasi, Dalia, Mintz, Michelle, Hathout, Yetrib, Vanderver, Adeline, Elroy-Stein, Orna
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2008
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2583043/
https://ncbi.nlm.nih.gov/pubmed/19023445
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0003783
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