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Lower Inhibitor Development in Hemophilia A Mice following Administration of Recombinant Factor VIII-O-Phospho-l-serine Complex

Factor VIII is a multidomain protein composed of A1, A2, B, A3, C1, and C2 domains. Deficiency or dysfunction of factor VIII causes hemophilia A, a bleeding disorder. Administration of exogenous recombinant factor VIII as a replacement leads to development of inhibitory antibodies against factor VII...

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Autors principals: Purohit, Vivek S., Ramani, Karthik, Sarkar, Rita, Kazazian, Haig H., Balasubramanian, Sathyamangalam V.
Format: Artigo
Idioma:Inglês
Publicat: 2005
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2582172/
https://ncbi.nlm.nih.gov/pubmed/15728582
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M500163200
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