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Domain Mapping of the Polycystin-2 C-terminal Tail Using de Novo Molecular Modeling and Biophysical Analysis

In polycystic kidney disease (PKD), polycystin-2 (PC2) is frequently mutated or truncated in the C-terminal cytoplasmic tail (PC2-C). The currently accepted model of PC2-C consists of an EF-hand motif overlapping with a short coiled coil; however, this model fails to explain the mechanisms by which...

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Autores principales: Ćelić, Andjelka, Petri, Edward T., Demeler, Borries, Ehrlich, Barbara E., Boggon, Titus J.
Formato: Artigo
Lenguaje:Inglês
Publicado: American Society for Biochemistry and Molecular Biology 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2568934/
https://ncbi.nlm.nih.gov/pubmed/18694932
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M802743200
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