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ATR protects the genome against CGG·CCG-repeat expansion in Fragile X premutation mice

Fragile X mental retardation syndrome is a repeat expansion disease caused by expansion of a CGG·CCG-repeat tract in the 5′ UTR of the FMR1 gene. In humans, small expansions occur more frequently on paternal transmission while large expansions are exclusively maternal in origin. It has been suggeste...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Entezam, Ali, Usdin, Karen
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Oxford University Press 2008
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC2241920/
https://ncbi.nlm.nih.gov/pubmed/18160412
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/nar/gkm1136
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