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Decay-accelerating factor is present on paroxysmal nocturnal hemoglobinuria erythroid progenitors and lost during erythropoiesis in vitro

A glycoprotein that regulates the deposition of C3b on the erythrocyte surface, called decay-accelerating factor or DAF, is absent from the red blood cells (RBC) of patients with paroxysmal nocturnal hemoglobinuria (PNH), explaining in part their abnormal sensitivity to complement. We used a specifi...

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Formato: Artigo
Lenguaje:Inglês
Publicado: The Rockefeller University Press 1985
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2187865/
https://ncbi.nlm.nih.gov/pubmed/2413153
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