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Mediating ERK1/2 signaling rescues congenital heart defects in a mouse model of Noonan syndrome

Noonan syndrome (NS) is an autosomal dominant disorder characterized by a wide spectrum of defects, which most frequently include proportionate short stature, craniofacial anomalies, and congenital heart disease (CHD). NS is the most common nonchromosomal cause of CHD, and 80%–90% of NS patients hav...

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Autori principali: Nakamura, Tomoki, Colbert, Melissa, Krenz, Maike, Molkentin, Jeffery D., Hahn, Harvey S., Dorn, Gerald W., Robbins, Jeffrey
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 2007
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1913487/
https://ncbi.nlm.nih.gov/pubmed/17641779
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1172/JCI30756
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