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Formation of native prions from minimal components in vitro

The conformational change of a host protein, PrP(C), into a disease-associated isoform, PrP(Sc), appears to play a critical role in the pathogenesis of prion diseases such as Creutzfeldt–Jakob disease and scrapie. However, the fundamental mechanism by which infectious prions are produced in neurons...

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Detalles Bibliográficos
Autores principales: Deleault, Nathan R., Harris, Brent T., Rees, Judy R., Supattapone, Surachai
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2007
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC1887554/
https://ncbi.nlm.nih.gov/pubmed/17535913
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0702662104
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