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A lamin A protein isoform overexpressed in Hutchinson–Gilford progeria syndrome interferes with mitosis in progeria and normal cells

Hutchinson–Gilford progeria syndrome (HGPS) is a rare genetic disorder characterized by dramatic premature aging. Classic HGPS is caused by a de novo point mutation in exon 11 (residue 1824, C → T) of the LMNA gene, activating a cryptic splice donor and resulting in a mutant lamin A (LA) protein ter...

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Autori principali: Cao, Kan, Capell, Brian C., Erdos, Michael R., Djabali, Karima, Collins, Francis S.
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2007
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC1821129/
https://ncbi.nlm.nih.gov/pubmed/17360355
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0611640104
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