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Successful treatment of carbohydrate deficient glycoprotein syndrome type 1b with oral mannose

An Asian girl presented with failure to thrive, congenital hepatic fibrosis, protein losing enteropathy, and hypoglycaemia. Phosphomannose isomerase activity in skin fibroblasts was reduced. She is homozygous for a mutation, D131N, in the phosphomannose isomerase gene (PM1), consistent with the diag...

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Detaylı Bibliyografya
Asıl Yazarlar: Hendriksz, C, McClean, P, Henderson, M, Keir, D, Worthington, V, Imtiaz, F, Schollen, E, Matthijs, G, Winchester, B
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: BMJ Group 2001
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC1718944/
https://ncbi.nlm.nih.gov/pubmed/11567948
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/adc.85.4.339
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