Hexacosenoyl-CoA is the most abundant very long-chain acyl-CoA in ATP binding cassette transporter D1-deficient cells[S]

X-linked adrenoleukodystrophy (X-ALD) is an inherited disorder caused by deleterious mutations in the ABCD1 gene. The ABCD1 protein transports very long-chain FAs (VLCFAs) from the cytosol into the peroxisome where the VLCFAs are degraded through β-oxidation. ABCD1 dysfunction leads to VLCFA accumul...

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Bibliografiske detaljer

Principais autores:	Kotaro Hama, Yuko Fujiwara, Shigeo Takashima, Yasuhiro Hayashi, Atsushi Yamashita, Nobuyuki Shimozawa, Kazuaki Yokoyama
Format:	Artigo
Sprog:	Inglês
Udgivet:	Elsevier 2020-04-01
Serier:	Journal of Lipid Research
Fag:	fatty acid fatty acid/metabolism lipids lipidomics peroxisomes very long-chain fatty acid
Online adgang:	http://www.sciencedirect.com/science/article/pii/S0022227520435023
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