Hexacosenoyl-CoA is the most abundant very long-chain acyl-CoA in ATP binding cassette transporter D1-deficient cells[S]

X-linked adrenoleukodystrophy (X-ALD) is an inherited disorder caused by deleterious mutations in the ABCD1 gene. The ABCD1 protein transports very long-chain FAs (VLCFAs) from the cytosol into the peroxisome where the VLCFAs are degraded through β-oxidation. ABCD1 dysfunction leads to VLCFA accumul...

Celý popis

Podrobná bibliografie

Hlavní autoři:	Kotaro Hama, Yuko Fujiwara, Shigeo Takashima, Yasuhiro Hayashi, Atsushi Yamashita, Nobuyuki Shimozawa, Kazuaki Yokoyama
Médium:	Artigo
Jazyk:	Inglês
Vydáno:	Elsevier 2020-04-01
Edice:	Journal of Lipid Research
Témata:	fatty acid fatty acid/metabolism lipids lipidomics peroxisomes very long-chain fatty acid
On-line přístup:	http://www.sciencedirect.com/science/article/pii/S0022227520435023
Tagy:	Přidat tag Žádné tagy, Buďte první, kdo vytvoří štítek k tomuto záznamu!