Hexacosenoyl-CoA is the most abundant very long-chain acyl-CoA in ATP binding cassette transporter D1-deficient cells[S]

X-linked adrenoleukodystrophy (X-ALD) is an inherited disorder caused by deleterious mutations in the ABCD1 gene. The ABCD1 protein transports very long-chain FAs (VLCFAs) from the cytosol into the peroxisome where the VLCFAs are degraded through β-oxidation. ABCD1 dysfunction leads to VLCFA accumul...

Ausführliche Beschreibung

Bibliografische Detailangaben

Hauptverfasser:	Kotaro Hama, Yuko Fujiwara, Shigeo Takashima, Yasuhiro Hayashi, Atsushi Yamashita, Nobuyuki Shimozawa, Kazuaki Yokoyama
Format:	Artigo
Sprache:	Inglês
Veröffentlicht:	Elsevier 2020-04-01
Schriftenreihe:	Journal of Lipid Research
Schlagworte:	fatty acid fatty acid/metabolism lipids lipidomics peroxisomes very long-chain fatty acid
Online-Zugang:	http://www.sciencedirect.com/science/article/pii/S0022227520435023
Tags:	Tag hinzufügen Keine Tags, Fügen Sie das erste Tag hinzu!