A novel mechanism involved in the coupling of mitochondrial biogenesis to oxidative phosphorylation

per Ostojić, Jelena, di Rago, Jean-Paul, Dujardin, Geneviève
Publicat a Microb Cell (2014)

Combining Inhibitor Resistance-conferring Mutations in Cytochrome b Creates Conditional Synthetic Lethality in Saccharomyces cerevisiae

per Ding, Martina G., di Rago, Jean-Paul, Trumpower, Bernard L.
Publicat 2009

Biochemical investigation of a human pathogenic mutation in the nuclear ATP5E gene using yeast as a model

per Sardin, Elodie, Donadello, Stéphanie, di Rago, Jean-Paul, Tetaud, Emmanuel
Publicat a Front Genet (2015)

A Genetic Screen Targeted on the F(O) Component of Mitochondrial ATP Synthase in Saccharomyces cerevisiae

per Godard, François, Tetaud, Emmanuel, Duvezin-Caubet, Stéphane, di Rago, Jean-Paul
Publicat 2011

Targeting Copper Homeostasis Improves Functioning of vps13Δ Yeast Mutant Cells, a Model of VPS13-Related Diseases

per Soczewka, Piotr, Tribouillard-Tanvier, Déborah, di Rago, Jean-Paul, Zoladek, Teresa, Kaminska, Joanna
Publicat a Int J Mol Sci (2021)

The two rotor components of yeast mitochondrial ATP synthase are mechanically coupled by subunit δ

per Duvezin-Caubet, Stéphane, Caron, Matthieu, Giraud, Marie-France, Velours, Jean, di Rago, Jean-Paul
Publicat 2003

Yeast Cells Depleted in Atp14p Fail to Assemble Atp6p within the ATP Synthase and Exhibit Altered Mitochondrial Cristae Morphology

per Goyon, Vanessa, Fronzes, Rémi, Salin, Bénédicte, di-Rago, Jean-Paul, Velours, Jean, Brèthes, Daniel
Publicat 2008

The depletion of F(1) subunit ε in yeast leads to an uncoupled respiratory phenotype that is rescued by mutations in the proton-translocating subunits of F(0)

per Tetaud, Emmanuel, Godard, François, Giraud, Marie-France, Ackerman, Sharon H., di Rago, Jean-Paul
Publicat 2014

ATP Synthase Diseases of Mitochondrial Genetic Origin

per Dautant, Alain, Meier, Thomas, Hahn, Alexander, Tribouillard-Tanvier, Déborah, di Rago, Jean-Paul, Kucharczyk, Roza
Publicat a Front Physiol (2018)

Regulation of Aerobic Energy Metabolism in Podospora anserina by Two Paralogous Genes Encoding Structurally Different c-Subunits of ATP Synthase

per Sellem, Carole H., di Rago, Jean-Paul, Lasserre, Jean-Paul, Ackerman, Sharon H., Sainsard-Chanet, Annie
Publicat a PLoS Genet (2016)

Consequences of the pathogenic T9176C mutation of human mitochondrial DNA on yeast mitochondrial ATP synthase

per Kucharczyk, Roza, Ezkurdia, Nahia, Couplan, Elodie, Procaccio, Vincent, Ackerman, Sharon H., Blondel, Marc, di Rago, Jean-Paul
Publicat 2010

Mitochondrial DNA Mutations Provoke Dominant Inhibition of Mitochondrial Inner Membrane Fusion

per Sauvanet, Cécile, Duvezin-Caubet, Stéphane, Salin, Bénédicte, David, Claudine, Massoni-Laporte, Aurélie, di Rago, Jean-Paul, Rojo, Manuel
Publicat 2012

Overexpression of mitochondrial oxodicarboxylate carrier (ODC1) preserves oxidative phosphorylation in a yeast model of Barth syndrome

per de Taffin de Tilques, Maxence, Tribouillard-Tanvier, Déborah, Tétaud, Emmanuel, Testet, Eric, di Rago, Jean-Paul, Lasserre, Jean-Paul
Publicat a Dis Model Mech (2017)

Molecular Basis of the Pathogenic Mechanism Induced by the m.9191T>C Mutation in Mitochondrial ATP6 Gene

per Su, Xin, Dautant, Alain, Godard, François, Bouhier, Marine, Zoladek, Teresa, Kucharczyk, Roza, di Rago, Jean-Paul, Tribouillard-Tanvier, Déborah
Publicat a Int J Mol Sci (2020)

MICOS and phospholipid transfer by Ups2–Mdm35 organize membrane lipid synthesis in mitochondria

per Aaltonen, Mari J., Friedman, Jonathan R., Osman, Christof, Salin, Bénédicte, di Rago, Jean-Paul, Nunnari, Jodi, Langer, Thomas, Tatsuta, Takashi
Publicat a J Cell Biol (2016)

Flavonoids as Potential Drugs for VPS13-Dependent Rare Neurodegenerative Diseases

per Soczewka, Piotr, Flis, Krzysztof, Tribouillard-Tanvier, Déborah, di Rago, Jean-Paul, Santos, Cláudia N., Menezes, Regina, Kaminska, Joanna, Zoladek, Teresa
Publicat a Genes (Basel) (2020)

The ATP synthase is involved in generating mitochondrial cristae morphology

per Paumard, Patrick, Vaillier, Jacques, Coulary, Bénédicte, Schaeffer, Jacques, Soubannier, Vincent, Mueller, David M., Brèthes, Daniel, di Rago, Jean-Paul, Velours, Jean
Publicat 2002

Introduction of cytochrome b mutations in Saccharomyces cerevisiae by a method that allows selection for both functional and nonfunctional cytochrome b proteins

per Ding, Martina G., Butler, Christine A., Saracco, Scott A., Fox, Thomas D., Godard, François, di Rago, Jean-Paul, Trumpower, Bernard L.
Publicat 2008

The pathogenic m.8993 T > G mutation in mitochondrial ATP6 gene prevents proton release from the subunit c-ring rotor of ATP synthase

per Su, Xin, Dautant, Alain, Rak, Malgorzata, Godard, François, Ezkurdia, Nahia, Bouhier, Marine, Bietenhader, Maïlis, Mueller, David M, Kucharczyk, Roza, di Rago, Jean-Paul, Tribouillard-Tanvier, Déborah
Publicat a Hum Mol Genet (2021)

Biochemical consequences of two clinically relevant ND-gene mutations in Escherichia coli respiratory complex I

per Nuber, Franziska, Schimpf, Johannes, di Rago, Jean-Paul, Tribouillard-Tanvier, Déborah, Procaccio, Vincent, Martin-Negrier, Marie-Laure, Trimouille, Aurélien, Biner, Olivier, von Ballmoos, Christoph, Friedrich, Thorsten
Publicat a Sci Rep (2021)